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An Open-label Phase II Study to Investigate the Efficacy, Safety, and Pharmacokinetics of Tirabrutinib in Patients With Primary Central Nervous System Lymphoma (PCNSL)

An Open-label Phase II Study to Investigate the Efficacy, Safety, and Pharmacokinetics of Tirabrutinib in Patients With Primary Central Nervous System Lymphoma (PCNSL)

  • Clinical Trial Information

    Trial Contact: Simoni, Christine; Frankos, Marie

    Trial Phone: 321.841.7293 ; 321.841.7303

  • IRB No: Pro00051026

    Protocol Abbrev: ONO-4059-09

    Principal Investigator: Alfredo Daniel Voloschin, MD

    Phase: Drug: Phase II

    Age Group: Adult

    Secondary Protocol No: ONO-4059-09

    Treatment: Experimental: Tirabrutinib monotherapy in patients with relapsed or refractory PCNSL (Part A) Patients with relapsed or refractory PCNSL who meet eligibility criteria will be enrolled to receive tirabrutinib monotherapy. Drug: Tirabrutinib Part A: Tirabrutinib 480 mg, taken orally, once a day on an empty stomach. Tirabrutinib treatment may be continued until disease progression or clinically unacceptable toxicity is observed. Other Name: ONO-4059 Experimental: Tirabrutinib + MTR in patients with newly diagnosed, treatment naïve PCNSL (Part B, Arm 1) Patients with newly diagnosed treatment naïve PCNSL who meet eligibility criteria will be enrolled to receive tirabrutinib + methotrexate/temozolomide/rituximab (MTR) Drug: Tirabrutinib Part B, Arm 1 - Tirabrutinib 320 mg or 480 mg, taken orally, once a day on an empty stomach in combination with an MTR induction regimen. Tirabrutinib with MTR treatment will be continued for 4 induction cycles (28-day/cycle), or until disease progression or clinically unacceptable toxicity is observed. For patients not receiving consolidation treatment following induction, tirabrutinib 480 mg will be continued until disease progression, unacceptable toxicities are observed, or the Investigator decides to stop treatment. Other Name: ONO-4059 Experimental: Tirabrutinib + R-MPV in patients with newly diagnosed, treatment naïve PCNSL (Part B, Arm 2) Patients with newly diagnosed treatment naïve PCNSL who meet eligibility criteria will be enrolled to receive tirabrutinib + rituximab/methotrexate/procarbazine/vincristine (R-MPV) Drug: Tirabrutinib Part B, Arm 2 - Tirabrutinib 320 mg or 480 mg, taken orally, once a day on an empty stomach in combination with an R-MPV induction regimen. Tirabrutinib with R-MPV treatment will be continued for 4 induction cycles (28-day/cycle), or until disease progression or clinically unacceptable toxicity is observed. For patients not receiving consolidation treatment following induction, tirabrutinib 480 mg will be continued until disease progression, unacceptable toxicities are observed, or the Investigator decides to stop treatment. Other Name: ONO-4059

    Therapies Involved: Oncology: 3rd line/Refractory

    ClinicalTrials.gov ID: NCT04947319

  • Objective

    To evaluate the efficacy of Tirabrutinib monotherapy in patients with R/R PCNSL.

  • Key Eligibility

    Inclusion Criteria (Part A)

    Written informed consent by the patient prior to screening
    Patients aged ≥ 18 years on the day of consenting to the study
    Pathologic diagnosis of PCNSL
    Relapse or refractory PCNSL with at least one prior HD MTX based therapy for PCNSL
    Measurable brain lesion with a minimum diameter > 1.0 cm in gadolinium enhanced magnetic resonance imaging (MRI) performed within 14 days before starting tirabrutinib treatment
    ECOG PS of 0, 1 or 2
    Life expectancy of at least 3 months
    Adequate bone marrow, renal, and hepatic function
    Inclusion Criteria (Part B)

    Written informed consent by the patient prior to screening
    Patients aged ≥ 18 years on the day of consenting to the study
    Pathologic diagnosis of PCNSL within the past 3 months
    No prior anti-tumor treatments for PCNSL
    Patients who, in the opinion of the Investigator, are suitable to receive treatment with a high dose methotrexate containing regimen
    Measurable brain lesion with a minimum diameter > 1.0 cm in gadolinium enhanced MRI performed within 14 days before starting study treatment
    ECOG PS of 0, 1 or 2
    Life expectancy of at least 6 months
    Adequate bone marrow, renal, and hepatic function
    Exclusion Criteria (Part A)

    Intraocular PCNSL with no brain lesion
    Patient who is intolerant of contrast enhanced MRI due to allergic reactions to contrast agents
    Patient with non-B cell PCNSL
    Patient with systemic presence of lymphoma
    Prior chemotherapy within 21 days, nitrosourea within 42 days, an antibody drug with anticancer activity (e.g., rituximab) within 28 days, prior radiotherapy within 14 days, prior major invasive surgery within 28 days, or allogeneic stem cell transplant within 6 months before starting tirabrutinib treatment
    Prior BTK inhibitor treatment
    Prior investigational drugs (including treatment in clinical research, unapproved combination products, and new dosage forms) within 28 days or 5 half-lives, whichever is shorter, before starting tirabrutinib treatment
    Concomitant systemic corticosteroid on an ongoing basis within 14 days before starting tirabrutinib treatment, with the exception of the following:

    Equivalent of up to 10 mg/day of prednisone for a disease other than PCNSL
    Equivalent of up to 50 mg/day of prednisone (equal to 8 mg/day of dexamethasone) for patients with lesions of the brain or spinal cord or both
    Patient who has received a CYP3A4 inducer or P-gp inducer within 14 days before starting tirabrutinib treatment
    Concomitant warfarin, any other warfarin derivative anticoagulant, vitamin K antagonists, novel oral anticoagulants, or antiplatelet therapy on an ongoing basis within 7 days before starting tirabrutinib treatment
    Active malignancy, other than PCNSL requiring systemic therapy
    Poorly controlled comorbidity, severe heart, severe lung disease, clinically significant liver diseases that could affect protocol compliance or safety or efficacy assessments
    Patient with bleeding diathesis
    Patients with a history of moderate or severe hepatic impairment
    QTcF > 480 milliseconds or requirement for ongoing treatment with concomitant medications that prolong the QT interval
    Active infection, including a HIV, cytomegalovirus infection or SARS-CoV-2, or has had, within 28 days before starting tirabrutinib treatment, an infection (other than nail trichophytosis) that requires hospitalization or an intravenous antibiotic
    Prior history of hypersensitivity or anaphylaxis to tirabrutinib
    Prior history of Stevens Johnson Syndrome or Toxic Epidermal Necrolysis
    Medical history of organ allografts
    Tests positive for HIV-1 antibody and HIV-2 antibody, human T-lymphotropic virus 1 antibody, HBs antigen, or HCV antibody. Tests positive for HBs antibody or hepatitis B virus core protein antibody and has a result of at least detectable in a hepatitis B virus deoxyribonucleic acid assay despite testing negative for HBs antigen.
    Patient is unable to swallow tablets; has malabsorption, malabsorption syndrome, or a comorbidity that affects gastric function; has undergone complete resection of the stomach or small intestine; has ulcerative colitis or symptomatic inflammatory bowel disease; or has partial or complete intestinal obstruction.
    Women who are pregnant or lactating
    Patient is found incapable of giving consent due to dementia or another such condition
    Patient is found to be otherwise ineligible for the study by the Investigator or sub-Investigator.
    Exclusion Criteria (Part B)

    Intraocular PCNSL with no brain lesion
    Patients for whom the selected backbone regimen medications (i.e, methotrexate/temozolomide/rituximab for MTR and rituximab/methotrexate/procarbazine/vincristine for R-MPV) are contraindicated
    Patients with a history of intolerable toxicity, hypersensitivity, anaphylaxis to the selected backbone regimen medications
    Patient who is intolerant of contrast enhanced MRI due to allergic reactions to contrast agents
    Patient with non-B cell PCNSL
    Patient with systemic presence of lymphoma
    Prior chemotherapy within 21 days, nitrosourea within 42 days, an antibody drug with anticancer activity (e.g., rituximab) within 28 days, prior radiotherapy within 14 days, prior major invasive surgery within 28 days, or allogeneic stem cell transplant within 6 months before starting tirabrutinib treatment
    Prior BTK inhibitor treatment
    Prior investigational drugs (including treatment in clinical research, unapproved combination products, and new dosage forms) within 28 days or 5 half-lives, whichever is shorter, before starting tirabrutinib treatment
    Concomitant systemic corticosteroid on an ongoing basis within 14 days before starting tirabrutinib treatment, with the exception of the following:

    Equivalent of up to 10 mg/day of prednisone for a disease other than PCNSL
    Equivalent of up to 50 mg/day of prednisone (equal to 8 mg/day of dexamethasone) for patients with lesions of the brain or spinal cord or both
    Patient who has received a CYP3A4 inducer or P-gp inducer within 14 days before starting tirabrutinib treatment
    Concomitant warfarin, any other warfarin derivative anticoagulant, vitamin K antagonists, novel oral anticoagulants, or antiplatelet therapy on an ongoing basis within 7 days before starting tirabrutinib treatment
    Active malignancy, other than PCNSL requiring systemic therapy
    Poorly controlled comorbidity, severe heart, severe lung disease, clinically significant liver diseases that could affect protocol compliance or safety or efficacy assessments
    Patient with bleeding diathesis
    Patients with a history of moderate or severe hepatic impairment
    QTcF > 480 milliseconds or requirement for ongoing treatment with concomitant medications that prolong the QT interval
    Active infection, including a HIV, cytomegalovirus infection or SARS-CoV-2, or has had, within 28 days before starting tirabrutinib treatment, an infection (other than nail trichophytosis) that requires hospitalization or an intravenous antibiotic
    Prior history of hypersensitivity or anaphylaxis to tirabrutinib
    Prior history of Stevens Johnson Syndrome or Toxic Epidermal Necrolysis
    Medical history of organ allografts
    Tests positive for HIV-1 antibody and HIV-2 antibody, human T-lymphotropic virus 1 antibody, HBs antigen, or HCV antibody. Tests positive for HBs antibody or hepatitis B virus core protein antibody and has a result of at least detectable in a hepatitis B virus deoxyribonucleic acid assay despite testing negative for HBs antigen.
    Patient is unable to swallow tablets; has malabsorption, malabsorption syndrome, or a comorbidity that affects gastric function; has undergone complete resection of the stomach or small intestine; has ulcerative colitis or symptomatic inflammatory bowel disease; or has partial or complete intestinal obstruction.
    Women who are pregnant or lactating
    Patient is found incapable of giving consent due to dementia or another such condition
    Patient is found to be otherwise ineligible for the study by the Investigator or sub-Investigator.